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Table 1 Proposed clinical classification for cherubism, modified from Raposo-Amaral classification[10]

From: Variable expressivity familial cherubism: woman transmitting cherubism without suffering the disease

Grade

Definition

0

Existence of the mutation without expression of the disease.

I

Lesion of the mandible without signs of root resorption

II

Lesions involving the mandible and maxilla without signs of root resorption

III

Aggressive lesion of the mandible with signs of root resorption

IV

Lesions involving the mandible and maxilla with signs of Root resorption

V

The rare, massively growing, aggressive, and extensively deforming juvenile lesions involving the maxilla and mandible

VI

The rare, massively growing, aggressive, and extensively deforming juvenile lesions involving the maxilla, mandible, and orbits